Clinical and morphological characteristics IgG4-associated retroperitoneal fibrosis
نویسندگان
چکیده
منابع مشابه
IgG4-associated multifocal systemic fibrosis complicating sclerosing sialadenitis, hypophysitis, and retroperitoneal fibrosis, but lacking pancreatic involvement.
A 71-year-old man was admitted with malaise, mild fever, anorexia, body weight loss, lower back pain, thirst, and polydipsia. He showed bilateral swelling of the submandibular glands. Examinations showed panhypopituitarism and a high serum IgG4 concentration. Fluorodeoxyglucose positron emission tomography (FDG-PET) revealed uptake in the pituitary gland, bilateral submandibular gland, bilatera...
متن کاملPathologically Proven Spontaneous Remission of IgG4-related Retroperitoneal Fibrosis
Some forms of idiopathic retroperitoneal fibrosis (RF) have recently been considered to be a part of the spectrum of immunoglobulin G4 (IgG4)-related disease. This case report is the first description of a spontaneous remission in a patient with pathologically proven IgG4-related RF. Although the pathogenesis and long-term disease behavior of IgG4-related RF remains unknown, we believe that an ...
متن کاملRapidly resolved IgG4-related retroperitoneal fibrosis after steroid pulse therapy
Retroperitoneal fibrosis (RF) is a disorder characterized by the presence of a retroperitoneal mass and concurrent systemic inflammation. Some cases of RF are recognized as belonging to the spectrum of immunoglobulin G4-related disease (IgG4-RD). Glucocorticoids are highly effective for treatment of retroperitoneal fibrosis, although the optimal dose and duration of therapy have not been establ...
متن کاملIdiopathic retroperitoneal fibrosis associated with an arteritis.
The first report in the world literature of the condition which is now generally known as idiopathic retroperitoneal fibrosis was that of Albarran (1905), but the first report in the English language did not appear until that of Ormond (1948). Since then many further case reports have been published, but the aetiology of the condition remains obscure. The disease usually presents as a urologica...
متن کاملAutoimmune pancreatitis associated with retroperitoneal fibrosis.
CONTEXT Autoimmune pancreatitis is sometimes associated with other autoimmune diseases. We have presented two cases of autoimmune pancreatitis with retroperitoneal fibrosis and compared our findings with those found in the literature. CASE 1: A 71-year-old male developed anorexia and weight loss. Abdominal ultrasonography (US) and computed tomography (CT) showed diffuse swelling of the pancreas...
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ژورنال
عنوان ژورنال: Almanac of Clinical Medicine
سال: 2020
ISSN: 2587-9294,2072-0505
DOI: 10.18786/2072-0505-2020-48-010